In a rare surgery performed on a 6-month-old patient from Iraq, the Paediatric Surgery team at Fortis Memorial Research Institute, Gurgaon headed by Dr Arvind Sabharwal (Director) performed a successful Whipple’s procedure for a rare genetic condition “Persistent Hyperinsulinemic Hypoglycemia of Infancy (PHHI)”. PHHI or nesidioblastoblastosis is an extremely rare hereditary disorder affecting 1 in 50,000 live births and is characterized by severe hypoglycaemia with elevated insulin levels due to excess secretion of insulin. If left untreated it causes irreversible brain damage or death due to hypoglycaemia in infants. Most babies are unresponsive to medical therapy and surgery in the form of near total pancreatectomy(removal of the pancreas in totality or practically) is the only cure.The Paediatric surgical team including Dr. Arvind Sabharwal and Dr. Anand Sinha decided to perform a complex Whipple’s surgery to remove the head of pancreas along with distal common bile duct and the duodenum (first part of the small intestine immediately beyond the stomach). The surgery lasting 4 hours was well tolerated by the child. The baby was discharged on full oral feeds, maintaining normal glucose levels without any supplements.
Article Source: https://www.fmri.in/ar/medical-bulletin/2-Year-old-kid-suffering-from-Gross-Congenital-Hydrocephalus-with-Megalencephaly-successfully-treated-at-Fortis-Gurgaon